Posterior Reversible Encephalopathy Syndrome after Steroid Pulse Therapy in Juvenile Dermatomyositis

Choi, Byung Woo; Oh, Seong-il; Oh, Kyung-Pil; Oh, Ki-Wook

Case report

Korean Journal of Neuromuscular Disorders 2015;7(2):85-88.

Byung Woo Choi, Seong-il Oh, Kyung-Pil Oh, Ki-Wook Oh

aDepartment of Neurology, Seoul Hospital, Hanyang University College of Medicine, Seoul; bDepartment of Neurology, Busan Paik Hospital, Inje University College of Medicine, Busan;

청소년 피부근염에서 스테로이드 정주 치료 후 발생한 가역적후뇌병증

최병우, 오성일, 오경필, 오기욱

한양대학교 의과대학 서울병원 신경과a, 인제대학교 의과대학 부산백병원 신경과b, 한양대학교 의과대학 구리병원 신경과c

Abstract

Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiological diagnosis characterized by seizures, headaches, lethargy, confusion, visual disturbances, and transient magnetic resonance imaging changes in the posterior circulation distribution. Juvenile dermatomyositis (JDM) is a rare but serious systemic autoimmune myopathy. We report a 17-year-old women with dermatomyositis who developed PRES after usual intravenous methylprednisolone treatment.